A
a
Here is a concise BGT (Bullet-Point Gist Tagline) summary:
BGT – Spontaneous Gastric Perforation (Paediatric, Beyond Neonatal Period)
Rare but life-threatening cause of acute abdomen in children beyond the neonatal period
Often idiopathic, but associated causes include:
Gastric wall ischemia / transmural necrosis
Connective tissue disorders (e.g. Ehlers-Danlos syndrome)
Eating disorders (acute gastric dilatation, anorexia nervosa)
Infection (rarely Candida)
Malignancy
Bezoars
Presents with:
Sudden severe abdominal pain
Distension
Vomiting
Pneumoperitoneum on imaging
Diagnosis frequently delayed due to non-specific early symptoms
Management principles:
Rapid resuscitation
Broad-spectrum antibiotics
Urgent surgical exploration
Repair or partial gastrectomy depending on necrosis
Mortality reported up to ~30% in some paediatric series
Prognosis linked to:
Degree of ischemia
Transmural necrosis
Preoperative physiological status
Consider underlying systemic pathology in atypical cases
High index of suspicion required in any child with acute abdomen + free air
No comments:
Post a Comment