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Gastrointestinal perforation is a rare but life-threatening complication in Duchenne Muscular Dystrophy (DMD).
Evidence limited to case reports and small series; no paediatric-specific guidelines identified.
Gastric and colonic perforations reported, often linked to bowel dysmotility and smooth muscle weakness.
High peri-operative risk due to cardiorespiratory compromise in DMD.
Both operative and non-operative management strategies described in high-risk patients.
Early recognition of acute abdominal symptoms is critical to reduce morbidity and mortality.
Multidisciplinary management essential (surgical, respiratory, cardiac, nutritional support).
Further research needed to guide paediatric risk stratification and management pathways.
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